A case of intravascular leiomyomatosis extending to inferior vena cava, right heart, and pulmonary artery.

Lee, Jong sim; Yoon, Jae won; Lee, Kyong hee; Jung, Sung Ho; Ryu, Young Joon; Park, Jeong Yeol

doi:2012.55.1.64

Case Report

Korean Journal of Obstetrics & Gynecology 2012;55(1):64-68.
DOI: https://doi.org/10.5468/KJOG.2012.55.1.64 Published online January 1, 2012.

A case of intravascular leiomyomatosis extending to inferior vena cava, right heart, and pulmonary artery.

Jong sim Lee, Jae won Yoon, Kyong hee Lee, Sung Ho Jung, Young Joon Ryu, Jeong Yeol Park

¹Department of Obstetrics and Gynecology, Asan Medical Center, University of Ulsan College of Medicine, Seoul, Korea. catgut1-0@hanmail.net
²Department of Thoracic and Cardiovascular Surgery, Asan Medical Center, University of Ulsan College of Medicine, Seoul, Korea.
³Department of Pathology, Asan Medical Center, University of Ulsan College of Medicine, Seoul, Korea.

Abstract

Intravascular leiomyomatosis is a rare entity of benign smooth muscle tumor invading into the lumen of veins. Although these tumors are histologically benign they sometimes extend into the cardiac cavity and can cause sudden death due to their incarceration into the artrioventricular orifice. We present a case of the intravascular leiomyomatosis originating from huge leiomyoma in the pelvic cavity and extending to the ovarian veins, the inferior vena cava, the right atrium, the right ventricle and the pulmonary artery. She underwent surgery by a single-stage o including laparotomy and venotomy without thoracotomy, and the tumor was successfully removed. Therefore, we report this case with a brief review of the literature.

Key Words: Intravascular leiomyomatosis, Heart extension, Single-stage operation