Congenital Absence of the Vagina and McIndoe Operation.

Yoo, Dal Young; Bang, Young Tae; Sun, Yun Soo; Kim, Yeon Heui; Kang, Jae Yul; Park, Young Sun

Obstet Gynecol Sci > Volume 40(6); 1997 > Article

Case Report

Korean Journal of Obstetrics & Gynecology 1997;40(6):1316-1320.
Published online: January 1, 2001

Congenital Absence of the Vagina and McIndoe Operation.

Dal Young Yoo, Young Tae Bang, Yun Soo Sun, Yeon Heui Kim, Jae Yul Kang, Young Sun Park

Department of Obstetrics and Gynecology, Eul-Ji General Hospital, Seoul, Korea.

Abstract

The Mayer-Rokitanski-Kuster-Hauser Syndrome refers to the clinical entity consistingof primary amenorrhea associated with congenital absence of the vagina, 46XX Karyotype,a rudimentary uterus in the form of bilateral noncanaliculated muscular band or completeabsence, normal ovarian function and normal ovulation, normal breast development, bodyproportion and body hair, frequent associated of renal, skeletal and other congenitalanomalies. A case of Mayer-Rokitanski-Kuster-Hauser syndrome was presented and the literatureswere reviewed briefly.

Keywords: Mayer-Rokitanski-Kuster-Hauser syndrome; McIndoe operation