A case of ovarian cancer developed in Mayer-Rokitansky-Kuster-Hauser syndrome: Innate carcinogenesis of ovarian cancer.

Ko, A Ra; Kim, Ji Hyun; Park, Sue Ye; Jeon, Young Eun; Kim, Sung Joo; Rhim, Chae Chun; Kang, Jung Bae; Park, Young Han

doi:2012.55.12.1001

Case Report

Korean Journal of Obstetrics & Gynecology 2012;55(12):1001-1005.
DOI: https://doi.org/10.5468/KJOG.2012.55.12.1001 Published online December 18, 2012.

A case of ovarian cancer developed in Mayer-Rokitansky-Kuster-Hauser syndrome: Innate carcinogenesis of ovarian cancer.

A Ra Ko, Ji Hyun Kim, Sue Ye Park, Young Eun Jeon, Sung Joo Kim, Chae Chun Rhim, Jung Bae Kang, Young Han Park

Department of Obstetrics and Gynecology, Hallym University College of Medicine, Chuncheon, Korea. drparkyh@yahoo.co.kr

Abstract

Vaginal aplasia is an unusual congenital anomaly of the genital tract with an incidence of 1 in 4,000 female births. The vast majority of the cases are part of Mayer-Rokitansky-Kuster-Hauser syndrome (MRKHs). In this syndrome, while the vagina is absent and the uterus is missing or extremely rudimentary, the ovarian function is normal and the secondary sexual characteristics are normally developed. The aim of the study is to present a case of ovarian cancer that developed on the ovary of a woman with MRKH syndrome.

Key Words: Mayer-Rokitansky-Kuster-Hauser syndrome, Ovarian cancer, Absent vagina