Prenatal Diagnosis of Exencephaly as a Consequence of an Amniotic Band Syndrome.

Oh, J H; Kim, M C; Park, K H; Choi, J W; Yang, S W; Cho, M Y

Original Article

Korean Journal of Obstetrics & Gynecology 1998;41(10):2668-2671.
Published online January 1, 2001.

Prenatal Diagnosis of Exencephaly as a Consequence of an Amniotic Band Syndrome.

J H Oh, M C Kim, K H Park, J W Choi, S W Yang, M Y Cho

Abstract

The amniotic band syndrome is a collection of fetal malformation associated with mesodermic fibrous bands that appear to entangle or entrap various fetal parts in utero, leading to deformation, malformation, or disruption. In about one third of cases, craniofacial deformities associated with amniotic band. Excencephaly is a precursor of anencephaly in which a large amount of brain tissue is present despite the absence of the calvaria. In exencephaly, destruction and disorganization of the developing brain ultimately result in the development of the anencephaly. We had experienced a case of exencephaly at early midtrimester by the amniotic band and presented with a brief review of literature.

Key Words: Amniotic band, Exencephaly