Asplenia(right atrial isomerism) diagnosed by prenatal ultrasonography: Report of One Case.

Yeon, Jung Eun; Yoo, Yong Gyun; Kang, Eun Joo; Hur, Hea Kyoung; Park, Dong Hee; Kim, Kyoung Seo; Hong, Sook Hee; Moon, Hwa Sook

Case Report

Korean Journal of Obstetrics & Gynecology 1999;42(9):2084-2087.
Published online January 1, 2001.

Asplenia(right atrial isomerism) diagnosed by prenatal ultrasonography: Report of One Case.

Jung Eun Yeon, Yong Gyun Yoo, Eun Joo Kang, Hea Kyoung Hur, Dong Hee Park, Kyoung Seo Kim, Sook Hee Hong, Hwa Sook Moon

Abstract

The syndromes of left atrial isomerism and right atrial isomerism, called polysplenia and asplenia syndromes, respectively, consist of congenital heart defects with disturbances in normal left right isometry, and the etiology of atrial isomerism remains unclear. Right atrial isomerism is traditionally associated with severe cardiac defects, especially complete atrioventricular septal defect, transposition of great arteries, pulmonary atresia, and total anomalous pulmonary venous return. Recently, we encountered one case of asplenia diagnosed by prenatal ultrasonography. We report a case with brief review of the literatures.

Key Words: Asplenia, prenatal ultrasonography