A  Case Report of Complete Testicular Feminization Syndrome with Rudimentary Salpinx.

Jo, Je Hun; Park, Young Bock; Park, Tae Hyoung; Jang, Won Yeon; Kim, Do Gyun; Kim, Kyoung Won; Kim, Dong Ki; Yoon, Hae Won; Kim, Dong Hun; Kim, Mi Woon; Park, Sung Tae

Case Report

Korean Journal of Obstetrics & Gynecology 2001;44(5):986-989.
Published online May 1, 2001.

A Case Report of Complete Testicular Feminization Syndrome with Rudimentary Salpinx.

Je Hun Jo, Young Bock Park, Tae Hyoung Park, Won Yeon Jang, Do Gyun Kim, Kyoung Won Kim, Dong Ki Kim, Hae Won Yoon, Dong Hun Kim, Mi Woon Kim, Sung Tae Park

¹Department of Obstetrics and Gynecology, College of Medicine, DongGuk University, Korea.
²Department of Pathology, College of Medicine, DongGuk University, Korea.
³Department of Anesthesiology, College of Medicine, DongGuk University, Korea.
⁴Department of Radiology, College of Medicine, DongGuk University, Korea.

Abstract

The Complete testicular feminization syndrome is a hereditary syndrome characterized clinically by female phenotype with 46, XY karyotype and bilateral testes. There is a congenital insensitivity to androgens, transmitted by means of a maternal X-linked recessive gene responsible for the androgen intracellular receptor. Therefore, androgen induction of Wolffian duct development does not occur. However, anti-mullerian hormone activity is present and the individual does not have mullerian development. Principle of treatment is reinforced to live normal female life. This is a case report of testicular feminization syndrome with rudimentary salpinx with the brief review of literatures.

Key Words: Complete testicular feminization syndrome, rudimentary salpinx