A Case of Malignant peripheral nerve sheath tumor of vulva.

Chang, Sun Min; Lee, Kyung Hee; Park, Man Chul; Lee, Yong Woo; Chae, Seoung Wan; Sohn, Jin Hee

Original Article

Korean Journal of Obstetrics & Gynecology 2001;44(8):1569-1572.
Published online August 1, 2001.

A Case of Malignant peripheral nerve sheath tumor of vulva.

Sun Min Chang, Kyung Hee Lee, Man Chul Park, Yong Woo Lee, Seoung Wan Chae, Jin Hee Sohn

¹Department of Obstetrics and Gynecology, College of Medicine, Hallym University, Seoul, Korea.
²Department of Pathology, College of Medicine, Hallym University, Seoul, Korea.

Abstract

Primary sarcomas of the vulva constitute an unusual groups of neoplasm. Peripheral nerve sheath tumor (Schwannoma) is arising from schwann cell of the neuroectodermal origin. This tumor arises on the cranial and spinal nerve roots, as well as on the course of the peripheral nerves rarely. In most cases this tumor is solitary but be multiple in Von Recklinghausen's disease. This initial treatment of this unusual tumor should be radical excision of the primary. Regional lymphadenectomy probably is not useful, since metastases are generally hematogenous rather than lymphatics. Radiation is ineffective as primary therapy

Key Words: peripheral nerve sheath tumor (schwannoma), sarcoma, vulva