A Case of Ovarian Mature Cystic Teratoma in Woman with Turner syndrome. |
Hyun Woo Nam, Jin Hee Lee, Yoon Sook Kim, Jong Soo Kim, Seung Do Choi, Dong Han Bae |
Department of Obstetrics and Gynecology, College of Medicine, Soonchunhyang University, Soonchunhyang Chunan Hospital, Chunan, Korea. IM_Doc@hotmail.com |
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Abstract |
Ovarian tumors in patients with Turner's syndrome are extremely rare. Turner syndrome occurs in 1 of 4000 to 10,000 live births, giving an approximate incidence of 1 to 2,500 live female births. Approximately half of the patients with Turner syndrome have "pure" 45,X cells in peripheral blood lymphocytes. Thirty to forty percents of Turner syndrome patients present mosaicism: 10-15% of the total group are 45,X/46,XX and 2 to 5% are 45,X/46,XY. In 45,X/46,XY Turner syndrome, the risk of developing a tumor is as high as 15-25%, with the possible development of dysgerminoma or gonadoblastoma. Recently, we experienced a case of a very rare left ovarian mature cystic teratoma in a 45,X/46,XX Turner syndrome, so report with a brief review of literature. |
Key Words:
Ovarian mature cystic teratoma, Turner syndrome |
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