A Case of Peritoneal Desmoplastic Small Round Cell Tumor which involved both ovaries.

Kim, Jun Kyung; Lee, Yun Sik; Ahn, Sun Nie; Shin, Hong Cheun; Lee, Chun June; Kim, Won Gyu; Kim, Weon

Case Report

Korean Journal of Obstetrics & Gynecology 2006;49(1):224-229.
Published online January 1, 2006.

A Case of Peritoneal Desmoplastic Small Round Cell Tumor which involved both ovaries.

Jun Kyung Kim, Yun Sik Lee, Sun Nie Ahn, Hong Cheun Shin, Chun June Lee, Won Gyu Kim, Weon Kim

¹Department of Obstetrics and Gynecology, Gospel Hospital, Kosin University, Busan, Korea. kwg@ns.kosinmed.or.kr
²Department of Medical Administration, KyungNam College of Information and Technology, Korea.

Abstract

Peritoneal desmoplastic small round cell tumor is a very rare malignant neoplasm and has specific clinical features; It is predominant in children and young males and has a well-demarcated large intra-abdominal tumor, which has not been associated with a primary visceral organ, with diffusely scattered multiple small tumors and rarely involves ovaries. It is a very aggressive and fast growing tumor along the peritoneal surfaces of the abdomen and pelvis. It has a typical histologic features and a specific immunohistochemical staining pattern. There is no definite treatment. It responses to surgery and chemotherapy at early period of therapy but relapses soon and rapidly progresses and then causes the death. We have experienced a peritoneal desmoplastic small round cell tumor which involved both ovaries, so we report this case with a brief review of literature.

Key Words: Desmoplastic small round cell tumor, Both ovaries