A case of peritoneal desmoplastic small round cell tumor.

Yang, Ki Yeol; Kim, Young Sun; Han, Ji Hyun; Park, Yong Ku; Jung, Min Hyung

Obstet Gynecol Sci > Volume 52(3); 2009 > Article

Case Report

Korean Journal of Obstetrics & Gynecology 2009;52(3):377-381.
Published online: March 1, 2009

A case of peritoneal desmoplastic small round cell tumor.

Ki Yeol Yang, Young Sun Kim, Ji Hyun Han, Yong Ku Park, Min Hyung Jung

¹Department of Obstetrics and Gynecology, Kyung Hee Medical Center, School of Medicine, Kyung Hee University, Seoul, Korea. webhospital@naver.com
²Department of Pathology, Kyung Hee Medical Center, School of Medicine, Kyung Hee University, Seoul, Korea.

Abstract

Desmoplastic small round cell tumor is a rare and aggressive tumor that affects young males. It is usually an abdominopelvic malignancy that demonstrates distinct histological appearances and a unique cytogenetic profile. There have been many different approaches to the treatment of desmoplastic small round cell tumor, but unfortunately it remains incurable and has poor long-term survival rates. However, with an aggressive approach to the treatment using multiple modalities, some temporary benefit to survival can be achieved. There has not yet been a case in which treatment has led to a curative outcome. Recently, we also experienced a case of very poor outcome of 31-year-old female with small round cell tumor in peritoneum. Here, we report the case with a brief review of literatures.

Keywords: Desmoplastic small round cell tumor; Peritoneum